Sturge-weber disease, a nonfamilial disorder results from a unilateral congenital capillary hemangioma invoving face and neck (facial nevus involving usually opthalmic division of trigeminal nerve) mucous memberane, meninges and choroid plexus.
Neurologic manifestations include seizures, mental defect, hemiparesis, or hemianopsia, rarely subarachnoid hemorrhage, glaucoma, and railroad track pattern of calcification on X-ray skull.
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